Folding Biology of Cystic Fibrosis: A Consortium-Based Approach to Disease

William E. Balch; Ineke Braakman; Jeff Brodsky; Raymond Frizzell; William Guggino; Gergely L. Lukacs; Christopher Penland; Harvey Pollard; William Skach; Eric Sorscher; Philip Thomas

doi:10.1002/9780470572702.ch19

Folding Biology of Cystic Fibrosis: A Consortium-Based Approach to Disease

William E. Balch^*
, Ineke Braakman
, Jeff Brodsky
, Raymond Frizzell
, William Guggino
, Gergely L. Lukacs
, Christopher Penland
, Harvey Pollard
, William Skach
, Eric Sorscher
, Philip Thomas

^*Corresponding author for this work

Anatomy, Physiology, and Genetics

Research output: Chapter in Book/Report/Conference proceeding › Chapter › peer-review

1 Scopus citations

Original language	English
Title of host publication	Protein Misfolding Diseases
Subtitle of host publication	Current and Emerging Principles and Therapies
Publisher	John Wiley and Sons
Pages	425-452
Number of pages	28
ISBN (Print)	9780471799283
DOIs	https://doi.org/10.1002/9780470572702.ch19
State	Published - 2 Jul 2010

Keywords

CFTR folding, series of sequential steps - nascent polypeptide, targeted to endoplasmic reticulum (ER)
Cystic fibrosis folding biology - consortium-based approach to disease
Trafficking to cell surface - "minimal export threshold" embracing key fundamental properties of protein fold-folding kinetics

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Balch, W. E., Braakman, I., Brodsky, J., Frizzell, R., Guggino, W., Lukacs, G. L., Penland, C., Pollard, H., Skach, W., Sorscher, E., & Thomas, P. (2010). Folding Biology of Cystic Fibrosis: A Consortium-Based Approach to Disease. In Protein Misfolding Diseases: Current and Emerging Principles and Therapies (pp. 425-452). John Wiley and Sons. https://doi.org/10.1002/9780470572702.ch19

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title = "Folding Biology of Cystic Fibrosis: A Consortium-Based Approach to Disease",

keywords = "CFTR folding, series of sequential steps - nascent polypeptide, targeted to endoplasmic reticulum (ER), Cystic fibrosis folding biology - consortium-based approach to disease, Trafficking to cell surface - {"}minimal export threshold{"} embracing key fundamental properties of protein fold-folding kinetics",

author = "Balch, \{William E.\} and Ineke Braakman and Jeff Brodsky and Raymond Frizzell and William Guggino and Lukacs, \{Gergely L.\} and Christopher Penland and Harvey Pollard and William Skach and Eric Sorscher and Philip Thomas",

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doi = "10.1002/9780470572702.ch19",

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T1 - Folding Biology of Cystic Fibrosis

T2 - A Consortium-Based Approach to Disease

AU - Balch, William E.

AU - Braakman, Ineke

AU - Brodsky, Jeff

AU - Frizzell, Raymond

AU - Guggino, William

AU - Lukacs, Gergely L.

AU - Penland, Christopher

AU - Pollard, Harvey

AU - Skach, William

AU - Sorscher, Eric

AU - Thomas, Philip

PY - 2010/7/2

Y1 - 2010/7/2

KW - CFTR folding, series of sequential steps - nascent polypeptide, targeted to endoplasmic reticulum (ER)

KW - Cystic fibrosis folding biology - consortium-based approach to disease

KW - Trafficking to cell surface - "minimal export threshold" embracing key fundamental properties of protein fold-folding kinetics

UR - https://www.scopus.com/pages/publications/80052630080

U2 - 10.1002/9780470572702.ch19

DO - 10.1002/9780470572702.ch19

M3 - Chapter

AN - SCOPUS:80052630080

SN - 9780471799283

SP - 425

EP - 452

BT - Protein Misfolding Diseases

PB - John Wiley and Sons

ER -

Folding Biology of Cystic Fibrosis: A Consortium-Based Approach to Disease

Keywords

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