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Type IV intestinal atresia, congenital bilateral perisylvian syndrome, and chronic pulmonary hypertension secondary to multiple vascular disruption syndrome in a monochorionic twin

  • Eveline H Shue
  • , Bruno Soares
  • , Jesse Courtier
  • , Jacob Hogue
  • , Thomas Shimotake
  • , Tippi C MacKenzie

Research output: Contribution to journalArticlepeer-review

2 Scopus citations

Abstract

We describe a rare case of multiple intestinal atresias, congenital bilateral perisylvian polymicrogyria, and chronic pulmonary hypertension in a surviving monochorionic twin with co-twin demise. This constellation of congenital anomalies represents a multiple vascular disruption syndrome due to intrauterine vascular compromise in the setting of possible twin-to-twin transfusion syndrome.

Original languageEnglish
Pages (from-to)1938-42
Number of pages5
JournalJournal of Pediatric Surgery
Volume47
Issue number10
DOIs
StatePublished - Oct 2012

Keywords

  • Abnormalities, Multiple
  • Chorion
  • Chronic Disease
  • Diseases in Twins/complications
  • Humans
  • Hypertension, Pulmonary/etiology
  • Infant, Newborn
  • Intellectual Disability/complications
  • Intestinal Atresia/classification
  • Male
  • Malformations of Cortical Development/complications
  • Syndrome
  • Vascular Diseases/complications

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