World's smallest combined en bloc liver-pancreas transplantation

Ahmed M. Elsabbagh; Jason Hawksworth; Khalid M. Khan; Nada Yazigi; Cal S. Matsumoto; Thomas M. Fishbein

doi:10.1111/petr.13082

World's smallest combined en bloc liver-pancreas transplantation

Ahmed M. Elsabbagh^*, Jason Hawksworth, Khalid M. Khan, Nada Yazigi, Cal S. Matsumoto, Thomas M. Fishbein

^*Corresponding author for this work

Research output: Contribution to journal › Article › peer-review

8 Scopus citations

Abstract

We present a case of a 2-year-old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin-dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children.

Original language	English
Article number	e13082
Journal	Pediatric Transplantation
Volume	22
Issue number	1
DOIs	https://doi.org/10.1111/petr.13082
State	Published - Feb 2018
Externally published	Yes

Keywords

Wolcott-Rallison syndrome
en bloc liver and pancreas transplant

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10.1111/petr.13082

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title = "World's smallest combined en bloc liver-pancreas transplantation",

abstract = "We present a case of a 2-year-old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin-dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children.",

keywords = "Wolcott-Rallison syndrome, en bloc liver and pancreas transplant",

author = "Elsabbagh, {Ahmed M.} and Jason Hawksworth and Khan, {Khalid M.} and Nada Yazigi and Matsumoto, {Cal S.} and Fishbein, {Thomas M.}",

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doi = "10.1111/petr.13082",

language = "English",

volume = "22",

journal = "Pediatric Transplantation",

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T1 - World's smallest combined en bloc liver-pancreas transplantation

AU - Elsabbagh, Ahmed M.

AU - Hawksworth, Jason

AU - Khan, Khalid M.

AU - Yazigi, Nada

AU - Matsumoto, Cal S.

AU - Fishbein, Thomas M.

PY - 2018/2

Y1 - 2018/2

N2 - We present a case of a 2-year-old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin-dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children.

AB - We present a case of a 2-year-old child who underwent a combined en bloc liver and pancreas transplant following complications of WRS. WRS is characterized clinically through infantile insulin-dependent diabetes mellitus, neutropenia, recurrent infections, propensity for liver failure following viral infections, bone dysplasia, and developmental delay. Usually, death occurs from fulminant liver and concomitant kidney failure. Few cases with WRS are reported in the literature, mostly from consanguineous parents. To the best of our knowledge, combined en bloc liver and pancreas transplant has not been performed in small children.

KW - Wolcott-Rallison syndrome

KW - en bloc liver and pancreas transplant

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DO - 10.1111/petr.13082

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SN - 1397-3142

VL - 22

JO - Pediatric Transplantation

JF - Pediatric Transplantation

IS - 1

M1 - e13082

ER -

World's smallest combined en bloc liver-pancreas transplantation

Abstract

Keywords

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